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DOID DOID:0050156
Name idiopathic pulmonary fibrosis
Definition An idiopathic interstitial pneumonia which is a distinctive type of chronic fibrosing interstitial pneumonia with thick scarring in the lung creating a honeycomb appearance. The main symptoms start insidiously as shortness of breath on exertion, cough, and diminished stamina. Other common complaints include weight loss and fatigue. The level of oxygen in the blood decreases, and the skin may take on a bluish tinge (called cyanosis) and the ends of the fingers may become thick or club-shape. In most people, symptoms worsen over a period ranging from about 6 months to several years.
http://www.merck.com/mmhe/sec04/ch050/ch050b.html?qt=idiopathic%20interstitial%20pneumonia&alt=sh, https://www.ncbi.nlm.nih.gov/pubmed/11790668
Xrefs

EFO:0000768

GARD:8609

ICD10CM:J84.112

ICD9CM:516.31

MESH:D054990

NCI:C35715

NCI:C35716

OMIM:178500

SNOMEDCT_US_2018_03_01:28168000

UMLS_CUI:C1800706

Subsets

NCIthesaurus

Synonyms

cryptogenic fibrosing alveolitis [EXACT]

FIBROCYSTIC PULMONARY DYSPLASIA [EXACT]

IDIOPATHIC PULMONARY FIBROSIS, FAMILIAL [EXACT]

Relationships

is_a idiopathic interstitial pneumonia

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