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Metadata
ID DOID:0050158
Name desquamative interstitial pneumonia
Definition An idiopathic interstitial pneumonia that is characterized by the accumulation of bronchiolocentric alveolar macrophages in alveolar spaces and interstitial inflammation and involves mild bronchiolar fibrosis and chronic inflammation.
http://ncit.nci.nih.gov/ncitbrowser/ConceptReport.jsp?dictionary=NCI_Thesaurus&version=14.10d&code=C35288, http://www.merck.com/mmhe/sec04/ch050/ch050b.html?qt=idiopathic%20interstitial%20pneumonia&alt=sh, https://www.ncbi.nlm.nih.gov/pubmed/11790668, https://www.ncbi.nlm.nih.gov/pubmed/16142185, https://www.ncbi.nlm.nih.gov/pubmed/16456642, https://www.ncbi.nlm.nih.gov/pubmed/23001799
Xrefs

ICD10CM:J84.117

ICD9CM:516.37

MESH:C562470

NCI:C35288

OMIM:263000

SNOMEDCT_US_2023_03_01:8549006

UMLS_CUI:C0238378

Alternateids

DOID:2796

Subsets

NCIthesaurus

Synonyms

familial desquamative interstitial pneumonitis [EXACT]

RBILD [EXACT]

respiratory bronchiolitis-associated interstitial lung disease [EXACT]

Parent Relationships

is_a idiopathic interstitial pneumonia

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