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Metadata
ID DOID:0050639
Name primary cutaneous amyloidosis
Definition An amyloidosis characterized by pruritus, skin scratching and by deposits of amyloid in the dermis.
https://www.ncbi.nlm.nih.gov/pubmed/19663869
Xrefs

GARD:132

OMIM:PS105250

ORDO:137807

ORDO:353220

Subsets

DO_rare_slim

Synonyms

familial primary localized cutaneous amyloidosis [EXACT]

PCA [EXACT]

Parent Relationships

is_a amyloidosis

is_a inherited metabolic disorder

is_a skin disease

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