Metadata | |
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ID | DOID:2097 |
Name | vulval Paget's disease |
Definition | A vulva adenocarcinoma that is characterized by distinctive large cells with prominent cytoplasm, referred to as Paget cells and is an intraepithelial neoplasm of epithelial origin expressing apocrine or eccrine glandular-like features. https://www.ncbi.nlm.nih.gov/pubmed/26971063 |
Xrefs |
SNOMEDCT_US_2023_03_01:254898001 |
Subsets |
NCIthesaurus |
Synonyms |
Paget's disease of vulva [EXACT] vulval Paget disease [EXACT] Vulvar Paget's disease [EXACT] |
Parent Relationships |
is_a vulva adenocarcinoma |