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Metadata
ID DOID:9212
Name pityriasis rubra pilaris
Definition A skin disease that is characterized by hyperkeratotic follicular papules coalescing into orange-red scaly plaques, islands of sparing, and palmoplantar keratoderma.
https://pubmed.ncbi.nlm.nih.gov/29302927/
Xrefs

GARD:7401

ICD10CM:L44.0

ICD9CM:696.4

MESH:D010916

NCI:C85014

OMIM:173200

SNOMEDCT_US_2023_03_01:3755001

UMLS_CUI:C0032027

Subsets

DO_rare_slim

NCIthesaurus

Synonyms

Devergie's disease [EXACT]

Parent Relationships

is_a skin disease

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