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Metadata
ID DOID:0080356
Name IgG4-related disease
Definition An autoimmune hypersensitivity disease that is characterized by tumefactive lesions, a dense lymphoplasmacytic infiltrate rich in IgG4-positive plasma cells, storiform fibrosis, obliterative phlebitis, autoimmune pancreatitis, and sometimes elevated serum IgG4 levels affecting various organs.
https://rarediseases.info.nih.gov/diseases/12521/index, https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4760655/, https://www.nejm.org/doi/full/10.1056/NEJMra1104650
Xrefs

GARD:12521

ORDO:284264

Parent Relationships

is_a autoimmune hypersensitivity disease

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