| Metadata | |
|---|---|
| ID | DOID:12236 |
| Name | primary biliary cholangitis |
| Definition | A liver cirrhosis characterized by chronic and slow progressive destruction of intrahepatic bile ducts. http://en.wikipedia.org/wiki/Primary_biliary_cirrhosis, http://www.merckmanuals.com/professional/hepatic_and_biliary_disorders/fibrosis_and_cirrhosis/primary_biliary_cirrhosis_pbc.html?qt=primary%20biliary%20cirrhosis&alt=sh, https://www.mayoclinic.org/diseases-conditions/primary-biliary-cholangitis-pbc/symptoms-causes/syc-20376874 |
| Xrefs |
EFO:0004267 SNOMEDCT_US_2023_03_01:1761006 SNOMEDCT_US_2023_03_01:31712002 |
| Alternateids |
DOID:1851 |
| Subsets |
DO_rare_slim NCIthesaurus |
| Synonyms |
biliary liver cirrhosis [EXACT] cholestatic cirrhosis [EXACT] chronic nonsuppurative destructive cholangitis [EXACT] primary biliary cirrhosis [EXACT] |
| Parent Relationships |
is_a primary immunodeficiency disease is_a liver cirrhosis |