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Metadata
ID DOID:4297
Name scimitar syndrome
Definition A congenital heart disease that is characterized by partial or entire anomalous curved venous drainage of the right lung to the inferior vena cava, association with variable right lung and pulmonary artery hypoplasia, dextraposition of the heart and an anomalous systemic blood supply to the ipsilateral lung.
https://en.wikipedia.org/wiki/Scimitar_syndrome, https://www.ncbi.nlm.nih.gov/pubmed/31536209
Xrefs

ICD10CM:Q26.8

MESH:D012587

NCI:C85056

OMIM:106700

ORDO:185

SNOMEDCT_US_2020_09_01:39905002

UMLS_CUI:C0036400

Subsets

NCIthesaurus

Synonyms

congenital venolobar syndrome [EXACT]

Halasz syndrome [EXACT]

hypogenetic lung syndrome [EXACT]

mirror-image lung syndrome [EXACT]

pulmonary venolobar syndrome [EXACT]

total anomalous pulmonary venous return [EXACT]

vena cava bronchovascular syndrome [EXACT]

Parent Relationships

is_a congenital heart disease

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