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Metadata
ID DOID:0050431
Name arrhythmogenic right ventricular cardiomyopathy
Definition An intrinsic cardiomyopathy that is characterized by hypokinetic areas involving the free wall of the right ventricle, with fibrofatty replacement of the right ventricular myocardium, with associated arrhythmias originating in the right ventricle and limited or no involvement of the left ventricle.
http://en.wikipedia.org/wiki/Arrhythmogenic_right_ventricular_dysplasia, http://ghr.nlm.nih.gov/condition/arrhythmogenic-right-ventricular-cardiomyopathy, http://my.clevelandclinic.org/services/heart/disorders/arvd, http://www.hopkinsmedicine.org/heart_vascular_institute/clinical_services/centers_excellence/arvd/patient_resources/questions.html, https://pubmed.ncbi.nlm.nih.gov/31637441/
Xrefs

MESH:D019571

NCI:C84571

OMIM:PS107970

ORDO:217656

ORDO:247

SNOMEDCT_US_2023_03_01:281170005

UMLS_CUI:C0349788

Subsets

DO_rare_slim

NCIthesaurus

Synonyms

arrhythmogenic right ventricular cardiomyopathy [EXACT]

arrhythmogenic right ventricular dysplasia [EXACT]

arrhythmogenic right ventricular dysplasia/cardiomyopathy [EXACT]

ARVC cardiomyopathy [EXACT]

ARVC [EXACT]

ARVD [EXACT]

right ventricular ACM [EXACT]

Parent Relationships

is_a intrinsic cardiomyopathy

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