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Metadata
ID DOID:0050594
PURL http://purl.obolibrary.org/obo/DOID_0050594 Copy
Name glycogen storage disease IX
Definition A glycogen storage disease characterized by deficiency of phosphorylase kinase (PhK) activity.
https://pubmed.ncbi.nlm.nih.gov/25266922/, https://www.ncbi.nlm.nih.gov/pubmed/17689125
Xrefs

MESH:C580130

MESH:D006015

NCI:C122662

ORDO:370

SNOMEDCT_US_2025_09_01:41527003

SNOMEDCT_US_2026_03_01:235908005

UMLS_CUI:C0017927

UMLS_CUI:C0268147

SKOS

exactMatch MESH:C580130

exactMatch ORDO:370

exactMatch NCI:C122662

exactMatch UMLS_CUI:C0268147

Alternateids

DOID:2751

Synonyms

glycogen storage disease 8 [EXACT]

glycogen storage disease 9 [EXACT]

glycogen storage disease type VIII [EXACT]

glycogen storage disease VIII [EXACT]

glycogenosis type IX [EXACT]

glycogenosis type VIII [EXACT]

GSD IX [EXACT]

GSD VIII [EXACT]

GSD8 [EXACT]

GSD9 [EXACT]

Parent Relationships

is_a glycogen storage disease

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