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Metadata
ID DOID:0050663
Name Bethlem myopathy
Definition A congenital muscular dystrophy that is characterized by myopathy and joint contractures that progresses slowly.
https://rarediseases.info.nih.gov/diseases/873/bethlem-myopathy
Xrefs

GARD:873

MESH:C535436

MIM:PS158810

NCI:C126688

ORDO:610

SNOMEDCT_US_2025_09_01:718572004

UMLS_CUI:C1834674

SKOS

exactMatch MIM:PS158810

narrowMatch ORDO:610

narrowMatch UMLS_CUI:C1834674

Subsets

DO_rare_slim

Synonyms

benign congenital muscular dystrophy [EXACT]

Parent Relationships

is_a congenital muscular dystrophy

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