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Metadata
ID DOID:0050710
Name 3-methylcrotonyl-CoA carboxylase deficiency
Definition An amino acid metabolic disorder that is classified by inadequate levels of the enzyme 3-methylcrotonyl-CoA carboxylase that helps break down proteins containing the amino acid leucine. This disease has_symptom muscular hypotonia (weak muscle tone), has_symptom muscular atrophy, has_symptom feeding difficulties, has_symptom recurrent episodes of vomiting and diarrhea, and has_symptom lethargy.
http://en.wikipedia.org/wiki/3-Methylcrotonyl-CoA_carboxylase_deficiency, http://omim.org/entry/210200
Xrefs

GARD:10954

OMIM:PS210200

ORDO:6

Subsets

DO_rare_slim

Synonyms

3-Methylcrotonylglycinuria [EXACT]

3MCC deficiency [EXACT]

BMCC deficiency [EXACT]

Parent Relationships

is_a amino acid metabolic disorder

is_a muscular disease

is_a autosomal recessive disease

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