Visualize Submit Comment
Metadata
ID DOID:0051029
PURL http://purl.obolibrary.org/obo/DOID_0051029 Copy
Name mitochondrial DNA depletion syndrome-21
Definition A mitochondrial DNA depletion syndrome that is characterized by ptosis, ophthalmoparesis, and myopathic limb weakness, as well as variable hepatopathy and altered T-lymphocyte profiles and that has_material_basis_in homozygous or compound heterozygous mutation in the GUK1 gene, which encodes guanylate kinase-1, on chromosome 1q42.
https://pubmed.ncbi.nlm.nih.gov/39230499/
Xrefs

MIM:621071

Parent Relationships

is_a mitochondrial DNA depletion syndrome

Add an item to the term tracker