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Metadata
ID DOID:0051059
Name autosomal recessive Segawa syndrome
Definition A dystonia that is characterized by onset in infancy of dopa-responsive dystonia and that has_material_basis_in homozygous or compound heterozygous mutation in the tyrosine hydroxylase gene (TH) on chromosome 11p15.
https://pubmed.ncbi.nlm.nih.gov/36568392/, https://pubmed.ncbi.nlm.nih.gov/22815559/
Xrefs

MIM:605407

ORDO:101150

Synonyms

autosomal recessive DOPA-responsive dystonia [EXACT]

Parent Relationships

is_a dystonia

is_a autosomal recessive disease

Subclass Logical Relationships

has material basis in some autosomal recessive inheritance

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