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Metadata
ID DOID:0051067
PURL http://purl.obolibrary.org/obo/DOID_0051067 Copy
Name Fontaine progeroid syndrome
Definition A progeroid syndrome that is characterized by poor growth, abnormal skeletal features, and distinctive craniofacial features with sagging, thin skin, and decreased subcutaneous fat suggesting an aged appearance that is most pronounced in infancy and improves with time and that has_material_basis_in heterozygous mutation in the SLC25A24 gene on chromosome 1p36.
https://pubmed.ncbi.nlm.nih.gov/35679445/, https://www.ncbi.nlm.nih.gov/books/NBK581082/
Xrefs

MIM:612289

ORDO:2095

ORDO:2963

ORDO:697101

Synonyms

Gorlin-Chaudhry-Moss syndrome [EXACT]

Progeroid Syndrome, Congenital, Petty Type [EXACT]

Parent Relationships

is_a autosomal dominant disease

is_a progeroid syndrome

Subclass Logical Relationships

has material basis in some autosomal dominant inheritance

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