| Metadata | |
|---|---|
| ID | DOID:0060704 |
| Name | lymphoproliferative syndrome |
| Definition | A primary immunodeficiency disease characterized by immune dysregulation typically after viral infection, usually associated with Epstein-Barr viral infection. https://www.ncbi.nlm.nih.gov/pubmed/198660, https://www.ncbi.nlm.nih.gov/pubmed/22197273 |
| Xrefs | |
| Subsets |
DO_rare_slim |
| Synonyms |
Combined immunodeficiency due to ITK deficiency [EXACT] |
| Parent Relationships |