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Metadata
ID DOID:0060842
PURL http://purl.obolibrary.org/obo/DOID_0060842 Copy
Name syndromic microphthalmia 16
Definition An isolated microphthalmia that is characterized by bilateral severe microphthalmia or anophthalmia with variable presence of midline defects, including cleft lip and palate, absence of frontal and/or sphenoidal sinuses, and absent pituitary gland and that has_material_basis_in compound heterozygous mutation in the RAX gene on chromosome 18q21.
https://pubmed.ncbi.nlm.nih.gov/30811539/, https://www.ncbi.nlm.nih.gov/pubmed/18783408, https://www.ncbi.nlm.nih.gov/pubmed/14662654
Xrefs

ICD10CM:Q11.0

MIM:611038

ORDO:2542

Subsets

DO_rare_slim

Synonyms

isolated microphthalmia 3 [EXACT]

MCOP3 [EXACT]

Parent Relationships

is_a syndromic microphthalmia

is_a autosomal recessive disease

Subclass Logical Relationships

has material basis in some autosomal recessive inheritance

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