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Metadata
ID DOID:0061119
PURL http://purl.obolibrary.org/obo/DOID_0061119 Copy
Name autosomal dominant tubulointerstitial kidney disease 4
Definition An autosomal dominant tubulointerstitial kidney disease characterized by early-onset anemia and increased serum uric acid with a bland urinalysis and without proteinuria that has_material_basis_in heterozygous mutation in the renin gene on chromosome 1q32.
https://pubmed.ncbi.nlm.nih.gov/19664745/
Xrefs

MIM:613092

ORDO:217330

Subsets

DO_rare_slim

Synonyms

familial juvenile hyperuricemic nephropathy 2 [EXACT]

Parent Relationships

is_a autosomal dominant tubulointerstitial kidney disease

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