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Metadata
ID DOID:0061231
PURL http://purl.obolibrary.org/obo/DOID_0061231 Copy
Name enhanced S-cone syndrome 1
Definition A retinal disease that is characterized by increased sensitivity to blue light; perception of blue light is mediated by what is normally the least populous cone photoreceptor subtype, the S (short wavelength, blue) cones and suffer visual loss, with night blindness occurring from early in life, varying degrees of L (long, red)- and M (middle, green)-cone vision, and retinal degeneration that has_material_basis_in homozygous or compound heterozygous mutation in the nuclear receptor gene NR2E3 on chromosome 15q23.
https://pubmed.ncbi.nlm.nih.gov/10655056/
Xrefs

MIM:268100

Parent Relationships

is_a enhanced S-cone syndrome

Subclass Logical Relationships

has material basis in some autosomal recessive inheritance

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