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Metadata
ID DOID:0070534
PURL http://purl.obolibrary.org/obo/DOID_0070534 Copy
Name arrhythmogenic left ventricular cardiomyopathy
Definition An intrinsic cardiomyopathy characterized by hypokinetic, non-dilated, fibrotic or fibrofatty left ventricular myocardium and ventricular arrhythmias with a right bundle branch block pattern, with limited to no involvement of the right ventricle.
https://pubmed.ncbi.nlm.nih.gov/31637441/
Xrefs

ORDO:293888

Subsets

DO_rare_slim

Synonyms

ALVC [EXACT]

left ventricular ACM [EXACT]

left-dominant arrhythmogenic cardiomyopathy [EXACT]

Parent Relationships

is_a intrinsic cardiomyopathy

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