| Metadata | |
|---|---|
| ID | DOID:0070662 |
| PURL | http://purl.obolibrary.org/obo/DOID_0070662 Copy |
| Name | subcutaneous panniculitis-like T-cell lymphoma |
| Definition | A primary cutaneous T-cell non-Hodgkin lymphoma characterized by infiltration of subcutaneous tissue by neoplastic alpha-beta cytotoxic T cells mimicking panniculitis. Homozygous or compound heterozygous mutation in the HAVCR2 gene may contribute to development of this disease, with some evidence of incomplete penetrance. https://pubmed.ncbi.nlm.nih.gov/19195975/, https://pubmed.ncbi.nlm.nih.gov/30374066/, https://www.ncbi.nlm.nih.gov/books/NBK538517/ |
| Xrefs |
ICDO:9708/3 SNOMEDCT_US_2025_09_01:404133000 |
| SKOS |
exactMatch ICD10CM:C86.3 exactMatch ICDO:9708/3 exactMatch MESH:C537503 exactMatch MIM:618398 exactMatch NCI:C6918 exactMatch ORDO:86884 exactMatch UMLS_CUI:C0522624 |
| Subsets |
DO_rare_slim NCIthesaurus |
| Synonyms |
SPTCL [EXACT] |
| Parent Relationships |