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Metadata
ID DOID:0070686
PURL http://purl.obolibrary.org/obo/DOID_0070686 Copy
Name X-linked congenital hydrocephalus
Definition A congenital hydrocephalus that has_material_basis_in homozygous mutation in the L1CAM gene on chromosome Xq28. Additional features include stenosis of the aqueduct of Sylvius, adducted thumbs, spastic paraparesis and impaired intellectual development.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10913327/, https://pubmed.ncbi.nlm.nih.gov/1303258/
Xrefs

GARD:434

MESH:C536078

MIM:307000

ORDO:2182

SNOMEDCT_US_2025_09_01:71779008

UMLS_CUI:C0265216

SKOS

exactMatch ORDO:2182

exactMatch MESH:C536078

exactMatch GARD:434

exactMatch UMLS_CUI:C0265216

exactMatch MIM:307000

Subsets

DO_rare_slim

Synonyms

X-linked hydrocephalus [EXACT]

Parent Relationships

is_a congenital hydrocephalus

is_a X-linked recessive disease

Subclass Logical Relationships

has material basis in some X-linked recessive inheritance

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