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Metadata
ID DOID:0070724
PURL http://purl.obolibrary.org/obo/DOID_0070724 Copy
Name dental radicular dysplasia
Definition A mouth disease characterized by taurodontism, unseparated roots, long roots, tooth agenesis, torus palatinus, and torus mandibularis that has_material_basis_in heterozygous mutation in the KCTD1 gene on chromosome 18q11.
https://pubmed.ncbi.nlm.nih.gov/38791218/
Xrefs

MIM:621434

SKOS

exactMatch MIM:621434

Subsets

DO_rare_slim

Synonyms

DNRD [EXACT]

Parent Relationships

is_a autosomal dominant disease

is_a mouth disease

Subclass Logical Relationships

has material basis in some autosomal dominant inheritance

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