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Metadata
ID DOID:0070733
PURL http://purl.obolibrary.org/obo/DOID_0070733 Copy
Name multiple mitochondrial dysfunctions syndrome 7
Definition A multiple mitochondrial dysfunctions syndrome characterized by a clinical spectrum ranging from neonatal fatal glycine encephalopathy to an attenuated phenotype of developmental delay, behavioral problems, limited epilepsy, and variable movement problems that has_material_basis_in homozygous or compound heterozygous mutation in the GCSH gene on chromosome 16q23.
https://pubmed.ncbi.nlm.nih.gov/36190515/
Xrefs

GARD:0026818

MIM:620423

UMLS_CUI:C5830586

SKOS

exactMatch MIM:620423

exactMatch UMLS_CUI:C5830586

exactMatch GARD:0026818

Subsets

DO_rare_slim

Synonyms

MMDS7 [EXACT]

Parent Relationships

is_a multiple mitochondrial dysfunctions syndrome

is_a autosomal recessive disease

Subclass Logical Relationships

has material basis in some autosomal recessive inheritance

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