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Metadata
ID DOID:0070750
PURL http://purl.obolibrary.org/obo/DOID_0070750 Copy
Name mitochondrial myopathy and ataxia
Definition A mitochondrial DNA depletion syndrome characterized by cerebellar ataxia, congenital muscle involvement with histologic findings ranging from myopathic to dystrophic, and pigmentary retinopathy that has_material_basis_in homozygous or compound heterozygous mutation in the MSTO1 gene on chromosome 1q22.
https://pubmed.ncbi.nlm.nih.gov/31463572/
Xrefs

MIM:617675

ORDO:502423

SNOMEDCT_US_2026_03_01:1237514002

UMLS_CUI:C4540096

SKOS

exactMatch ORDO:502423

exactMatch MIM:617675

exactMatch UMLS_CUI:C4540096

Subsets

DO_rare_slim

Parent Relationships

is_a mitochondrial DNA depletion syndrome

is_a mitochondrial myopathy

is_a autosomal recessive disease

Subclass Logical Relationships

has material basis in some autosomal recessive inheritance

has phenotype some Mitochondrial depletion

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