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Metadata
ID DOID:0070757
PURL http://purl.obolibrary.org/obo/DOID_0070757 Copy
Name Pilarowski-Bjornsson syndrome
Definition An autosomal dominant intellectual developmental disorder characterized by delayed development, impaired intellectual development, speech apraxia, and mild dysmorphic features that has_material_basis_in heterozygous mutation in the CHD1 gene on chromosome 5q.
https://pubmed.ncbi.nlm.nih.gov/28866611/
Xrefs

GARD:0017970

ICD10CM:Q87.0

MIM:617682

ORDO:529965

SNOMEDCT_US_2026_03_01:1217382002

UMLS_CUI:C4540131

SKOS

exactMatch MIM:617682

exactMatch GARD:0017970

exactMatch ORDO:529965

exactMatch UMLS_CUI:C4540131

broadMatch ICD10CM:Q87.0

Subsets

DO_rare_slim

Parent Relationships

is_a autosomal dominant intellectual developmental disorder

Subclass Logical Relationships

has material basis in some autosomal dominant inheritance

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