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Metadata
ID DOID:0070763
PURL http://purl.obolibrary.org/obo/DOID_0070763 Copy
Name primary ciliary dyskinesia 50
Definition A primary ciliary dyskinesia characterized by chronic sinusitis, bronchitis, and male infertility with markedly reduced progressive motility and multiple morphologic abnormalities of the flagella resulting from defects or loss of the inner dynein arms of the sperm flagella that has_material_basis_in homozygous or compound heterozygous mutation in the DNAH7 gene on chromosome 2q32.
https://pubmed.ncbi.nlm.nih.gov/34476482/, https://pubmed.ncbi.nlm.nih.gov/35543642/, https://www.ncbi.nlm.nih.gov/books/NBK1122/
Xrefs

MIM:620356

UMLS_CUI:C5830473

SKOS

exactMatch MIM:620356

exactMatch UMLS_CUI:C5830473

Subsets

DO_rare_slim

Synonyms

CILD50 [EXACT]

Parent Relationships

is_a autosomal recessive disease

is_a primary ciliary dyskinesia

Subclass Logical Relationships

has material basis in some autosomal recessive inheritance

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