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Metadata
ID DOID:0070767
PURL http://purl.obolibrary.org/obo/DOID_0070767 Copy
Name primary ciliary dyskinesia 54
Definition A primary ciliary dyskinesia characterized by a mild respiratory phenotype including rhinitis, sinusitis, asthma, and bronchiectasis that has_material_basis_in compound heterozygous mutation in the CFAP54 gene on chromosome 12q23. Some abnormalities of spermatozoa have been reported, but their effect on male fertility is unclear.
https://pubmed.ncbi.nlm.nih.gov/37725231/
Xrefs

MIM:621125

UMLS_CUI:C6012704

SKOS

exactMatch UMLS_CUI:C6012704

exactMatch MIM:621125

Subsets

DO_rare_slim

Synonyms

CILD54 [EXACT]

Parent Relationships

is_a autosomal recessive disease

is_a primary ciliary dyskinesia

Subclass Logical Relationships

has material basis in some autosomal recessive inheritance

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