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Metadata
ID DOID:0070789
PURL http://purl.obolibrary.org/obo/DOID_0070789 Copy
Name cataract, alopecia, oral mucosal disorder, and psoriasis-like syndrome
Definition A syndrome characterized by early-onset lens cataract, generalized nonscarring alopecia, oral mucosal disorder, and severe psoriasiform skin lesions affecting the scalp, facial, inguinal region, buttocks and lower extremities that has_material_basis_in compound heterozygous mutation in the MBTPS1 gene on chromosome 1p21.
https://pubmed.ncbi.nlm.nih.gov/35362222/
Xrefs

MIM:621252

UMLS_CUI:C6012743

SKOS

exactMatch MIM:621252

exactMatch UMLS_CUI:C6012743

Subsets

DO_rare_slim

Synonyms

CAOP [EXACT]

CAOP syndrome [EXACT]

Parent Relationships

is_a syndrome

is_a autosomal recessive disease

Subclass Logical Relationships

has material basis in some autosomal recessive inheritance

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