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Metadata
ID DOID:0070794
PURL http://purl.obolibrary.org/obo/DOID_0070794 Copy
Name Guillouet-Gordon syndrome
Definition A syndrome characterized by intellectual disability, speech delay, and/or motor delay of variable severity associated with variable combinations of craniofacial defects, anomalies of the extremities, and heart defects that has_material_basis_in homozygous or compound heterozygous mutation in the MED16 gene on chromosome 19p13.
https://pubmed.ncbi.nlm.nih.gov/40081376/
Xrefs

MIM:621220

UMLS_CUI:C6012729

SKOS

exactMatch UMLS_CUI:C6012729

exactMatch MIM:621220

Subsets

DO_rare_slim

Synonyms

GGNS [EXACT]

Parent Relationships

is_a syndrome

is_a autosomal recessive disease

Subclass Logical Relationships

has material basis in some autosomal recessive inheritance

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