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Metadata
ID DOID:0070796
PURL http://purl.obolibrary.org/obo/DOID_0070796 Copy
Name ICHAD syndrome
Definition An immune system disease characterized by onset of immunodysregulation, craniofacial anomalies, hearing impairment, athelia, and developmental delay soon after birth or in early infancy that has_material_basis_in heterozygous gain-of-function mutation in the IKZF2 gene on chromosome 2q34. Affected individuals have recurrent, mainly respiratory, infections and may have autoimmune features.
https://pubmed.ncbi.nlm.nih.gov/37316189/
Xrefs

MIM:621234

ORDO:699599

UMLS_CUI:C6012290

SKOS

exactMatch UMLS_CUI:C6012290

exactMatch ORDO:699599

exactMatch MIM:621234

Subsets

DO_rare_slim

Synonyms

ICHAD [EXACT]

immunodysregulation, craniofacial anomalies, hearing impairment, athelia, and developmental delay [EXACT]

Parent Relationships

is_a autosomal dominant disease

is_a immune system disease

Subclass Logical Relationships

has phenotype some Absent nipple

has material basis in some autosomal dominant inheritance

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