| Metadata | |
|---|---|
| ID | DOID:0080356 |
| Name | IgG4-related disease |
| Definition | An autoimmune disease that is characterized by tumefactive lesions, a dense lymphoplasmacytic infiltrate rich in IgG4-positive plasma cells, storiform fibrosis, obliterative phlebitis, autoimmune pancreatitis, and sometimes elevated serum IgG4 levels affecting various organs. https://rarediseases.info.nih.gov/diseases/12521/index, https://www.ncbi.nlm.nih.gov/articles/PMC4760655/, https://www.nejm.org/doi/full/10.1056/NEJMra1104650 |
| Xrefs | |
| Subsets |
DO_rare_slim |
| Parent Relationships |
is_a autoimmune disease |