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Metadata
ID DOID:0080511
PURL http://purl.obolibrary.org/obo/DOID_0080511 Copy
Name generalized intermediate epidermolysis bullosa simplex 1B
Definition An epidermolysis bullosa simplex that is characterized by widespread blisters that appear at birth or in early infancy and has_material_basis_in heterozygous mutation in the KRT14 gene on chromosome 17q21.
https://ghr.nlm.nih.gov/condition/epidermolysis-bullosa-simplex#resources, https://pubmed.ncbi.nlm.nih.gov/32017015/
Xrefs

MIM:131900

Synonyms

epidermolysis bullosa simplex generalized type [EXACT]

epidermolysis bullosa simplex Koebner type [EXACT]

Parent Relationships

is_a autosomal dominant disease

is_a epidermolysis bullosa simplex

Subclass Logical Relationships

existence starts during some Infantile onset

has material basis in some autosomal dominant inheritance

existence starts during some Congenital onset

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