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Metadata
ID DOID:0081123
Name X-linked mental retardation Gustavson type
Definition A syndromic X-linked intellectual disability that is characterized by intrauterine growth retardation, microcephaly, hypotonia, and severe global developmental delay, usually resulting in death in infancy or early childhood that has_material_basis_in hemizygous mutation in the RBMX gene on chromosome Xq26.
https://pubmed.ncbi.nlm.nih.gov/37277488/
Xrefs

GARD:5611

MIM:309555

ORDO:3078

Subsets

DO_rare_slim

Synonyms

Gustavson type of X-linked syndromic intellectual developmental disorder [EXACT]

mental retardation with optic atrophy, deafness and seizures [EXACT]

Parent Relationships

is_a syndromic X-linked intellectual disability

Subclass Logical Relationships

has material basis in some X-linked inheritance

existence starts during some Infantile onset

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