Metadata | |
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ID | DOID:0081259 |
Name | desmoplastic infantile ganglioglioma / desmoplastic infantile astrocytoma |
Definition | A ganglioglioma occurring predominantly in the cerebral hemispheres of infants, that are driven by MAPK pathway activation and composed of a mixed astrocytic and neuronal component (DIG) or an astrocytic component only (DIA) embedded in an extensive desmoplastic stroma, often containing foci of undifferentiated embryonal-like tumour cells. https://pubmed.ncbi.nlm.nih.gov/35015431/, https://pubmed.ncbi.nlm.nih.gov/31223403/ |
Xrefs |
ICDO:9412/1 |
Subsets |
DO_cancer_slim DO_childhood_cancer_slim NCIthesaurus |
Synonyms |
Desmoplastic Infantile Astrocytoma [EXACT] desmoplastic infantile ganglioglioma and desmoplastic infantile astrocytoma [EXACT] desmoplastic infantile ganglioglioma [EXACT] |
Parent Relationships |
is_a ganglioglioma |
Subclass Logical Relationships |
existence starts during some Infantile onset |