| Metadata | |
|---|---|
| ID | DOID:0081259 |
| Name | desmoplastic infantile ganglioglioma / desmoplastic infantile astrocytoma |
| Definition | A ganglioglioma occurring predominantly in the cerebral hemispheres of infants, that are driven by MAPK pathway activation and composed of a mixed astrocytic and neuronal component (DIG) or an astrocytic component only (DIA) embedded in an extensive desmoplastic stroma, often containing foci of undifferentiated embryonal-like tumour cells. https://pubmed.ncbi.nlm.nih.gov/35015431/, https://pubmed.ncbi.nlm.nih.gov/31223403/ |
| Xrefs |
ICDO:9412/1 |
| Subsets |
DO_cancer_slim DO_childhood_cancer_slim NCIthesaurus |
| Synonyms |
Desmoplastic Infantile Astrocytoma [EXACT] desmoplastic infantile ganglioglioma and desmoplastic infantile astrocytoma [EXACT] desmoplastic infantile ganglioglioma [EXACT] |
| Parent Relationships |
is_a ganglioglioma |
| Subclass Logical Relationships |
existence starts during some Infantile onset |