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Metadata
ID DOID:0110195
PURL http://purl.obolibrary.org/obo/DOID_0110195 Copy
Name congenital hypomyelinating neuropathy 1
Definition A congenital hypomyelinating neuropathy that has_material_basis_in homozygous or heterozygous mutation in the EGR2 gene on chromosome 10q21.
https://www.ncbi.nlm.nih.gov/pubmed/9537424
Xrefs

ICD10CM:G60.0

MIM:605253

ORDO:99951

SNOMEDCT_US_2025_09_01:763135001

UMLS_CUI:C4721437

SKOS

exactMatch ORDO:99951

exactMatch MIM:605253

exactMatch UMLS_CUI:C4721437

broadMatch ICD10CM:G60.0

Subsets

DO_rare_slim

Synonyms

autosomal recessive congenital hypomyelinating or amyelinating neuropathy [EXACT]

Charcot-Marie-Tooth disease type 4E [EXACT]

Charcot-Marie-Tooth neuropathy type 4E [EXACT]

CHN1 [EXACT]

CMT4E [EXACT]

Neuropathy, congenital hypomyelinating, 1 [EXACT]

Parent Relationships

is_a autosomal dominant disease

is_a Charcot-Marie-Tooth disease type 4

is_a autosomal recessive disease

is_a congenital hypomyelinating neuropathy

Subclass Logical Relationships

has material basis in some autosomal dominant inheritance

has material basis in some autosomal recessive inheritance

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