Metadata | |
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ID | DOID:0110721 |
Name | neuronal ceroid lipofuscinosis 1 |
Definition | A neuronal ceroid lipofuscinosis that is characterized by variable age of onset of symptoms (progressive dementia, seizures, and progressive visual failure) and lipopigment pattern of granular osmiophilic deposits, and has_material_basis_in homozygous or compound heterozygous mutation in the PPT1 gene on chromosome 1p34. https://www.ncbi.nlm.nih.gov/pubmed/7637805 |
Xrefs | |
Subsets |
DO_rare_slim |
Synonyms |
CLN1 [EXACT] neuronal ceroid lipofuscinosis 1 variable age of onset [EXACT] |
Parent Relationships | |
Subclass Logical Relationships |
has symptom some seizure has material basis in some autosomal recessive inheritance |