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Metadata
ID DOID:0111152
Name multicentric Castleman disease
Definition A Castleman disease characterized by systemic inflammatory symptoms, polyclonal lymphoproliferation, cytopenias, and multiple organ system dysfunction caused by a cytokine storm often including interleukin-6.
http://www.bloodjournal.org/content/129/12/1646, https://rarediseases.info.nih.gov/diseases/9644/multicentric-castleman-disease
Xrefs

GARD:9644

MESH:C537372

NCI:C27855

ORDO:93686

SNOMEDCT_US_2023_03_01:1156805003

UMLS_CUI:C1334815

Subsets

DO_rare_slim

NCIthesaurus

Synonyms

MCD [EXACT]

multicentric giant lymph node hyperplasia [EXACT]

plasmablastic multicentric Castleman disease [EXACT]

PMCD [EXACT]

Parent Relationships

is_a Castleman disease

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