| Metadata | |
|---|---|
| ID | DOID:0111152 |
| Name | multicentric Castleman disease |
| Definition | A Castleman disease characterized by systemic inflammatory symptoms, polyclonal lymphoproliferation, cytopenias, and multiple organ system dysfunction caused by a cytokine storm often including interleukin-6. http://www.bloodjournal.org/content/129/12/1646, https://rarediseases.info.nih.gov/diseases/9644/multicentric-castleman-disease |
| Xrefs |
SNOMEDCT_US_2023_03_01:1156805003 |
| Subsets |
DO_rare_slim NCIthesaurus |
| Synonyms |
MCD [EXACT] multicentric giant lymph node hyperplasia [EXACT] plasmablastic multicentric Castleman disease [EXACT] PMCD [EXACT] |
| Parent Relationships |
is_a Castleman disease |
| Subclass Logical Relationships |
has symptom some cytopenia |