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Metadata
ID DOID:0111340
Name dominant optic atrophy plus syndrome
Definition A syndrome characterized by visual loss and sensorineural hearing loss with onset in childhood and associated with other symptoms including; progressive external ophthalmoplegia, muscle cramps, hyperreflexia, and ataxia that has_material_basis_in heterozygous mutation in the OPA1 gene on chromosome 3q29.
https://www.ncbi.nlm.nih.gov/pubmed/12566046, https://www.ncbi.nlm.nih.gov/pubmed/20157015
Xrefs

GARD:5243

OMIM:125250

SNOMEDCT_US_2023_03_01:715374003

UMLS_CUI:C3276549

Subsets

DO_rare_slim

Synonyms

DOA+ [EXACT]

optic atrophy with or without deafness, ophthalmoplegia, myopathy, ataxia, and neuropathy [EXACT]

Parent Relationships

is_a syndrome

is_a autosomal dominant disease

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