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Metadata
ID DOID:0111456
Name Kaufman oculocerebrofacial syndrome
Definition A syndromic intellectual disability characterized by developmental delay, growth retardation with a small head circumference, facial dysmorphisms, and low cholesterol levels that has_material_basis_in homozygous or compound heterozygous mutation in the UBE3B gene on chromosome 12q24.11.
https://ghr.nlm.nih.gov/condition/kaufman-oculocerebrofacial-syndrome, https://www.ncbi.nlm.nih.gov/pubmed/23200864
Xrefs

GARD:3084

MESH:C537013

MIM:244450

ORDO:2707

SNOMEDCT_US_2023_03_01:722056009

UMLS_CUI:C1855663

Subsets

DO_rare_slim

Synonyms

blepharophimosis ptosis intellectual disability syndrome [EXACT]

oculocerebrofacial syndrome, Kaufman type [EXACT]

Parent Relationships

is_a syndromic intellectual disability

is_a autosomal recessive disease

Subclass Logical Relationships

has phenotype some Neurodevelopmental delay

has material basis in some autosomal recessive inheritance

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