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Metadata
ID DOID:0112011
Name mutilating palmoplantar keratoderma with periorificial keratotic plaques
Definition A keratosis characterized by a bilateral mutilating palmoplantar keratoderma and periorificial keratotic plaques with severe pruritus of lesions.
https://pubmed.ncbi.nlm.nih.gov/16227106/, https://pubmed.ncbi.nlm.nih.gov/17367233/, https://pubmed.ncbi.nlm.nih.gov/22405088/
Xrefs

GARD:4075

MEDDRA:10068842

ORDO:659

Subsets

DO_rare_slim

Synonyms

mutilating palmoplantar hyperkeratosis with periorificial keratotic plaques [EXACT]

OLMS [EXACT]

Olmsted syndrome [EXACT]

palmoplantar and periorificial keratoderma [EXACT]

Parent Relationships

is_a keratosis

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