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Metadata
ID DOID:0112136
Name severe congenital neutropenia 4
Definition A severe congenital neutropenia that has_material_basis_in homozygous or compound heterozygous mutation in the G6PC3 gene on chromosome 17q21.31.
https://pubmed.ncbi.nlm.nih.gov/19118303/
Xrefs

MIM:612541

ORDO:331176

Subsets

DO_rare_slim

Synonyms

autosomal recessive severe congenital neutropenia due to G6PC3 deficiency [EXACT]

Dursun syndrome [EXACT]

SCN4 [EXACT]

severe congenital neutropenia-pulmonary hypertension-superficial venous angiectasis syndrome [EXACT]

Parent Relationships

is_a severe congenital neutropenia

is_a autosomal recessive disease

Subclass Logical Relationships

has material basis in some autosomal recessive inheritance

disease has basis in some Abnormality of prenatal development or birth

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