Visualize Submit Comment
Metadata
ID DOID:0112296
PURL http://purl.obolibrary.org/obo/DOID_0112296 Copy
Name spondylometaphyseal dysplasia Algerian type
Definition A spondylometaphyseal dysplasia characterized by a short trunk and severe genu valgum and that has_material_basis_in heterozygous mutation in the COL2A1 gene on chromosome 12q13.
https://pubmed.ncbi.nlm.nih.gov/23653587/, https://pubmed.ncbi.nlm.nih.gov/3368247/
Xrefs

GARD:504

MESH:C535794

MIM:184253

ORDO:93316

SNOMEDCT_US_2025_09_01:719304005

UMLS_CUI:C1866688

Subsets

DO_rare_slim

Synonyms

spondylometaphyseal dysplasia with severe genu valgum [EXACT]

spondylometaphyseal dysplasia, Schmidt type [EXACT]

Parent Relationships

is_a spondylometaphyseal dysplasia

Add an item to the term tracker