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Metadata
ID DOID:12236
Name primary biliary cholangitis
Definition A liver cirrhosis characterized by chronic and slow progressive destruction of intrahepatic bile ducts.
http://en.wikipedia.org/wiki/Primary_biliary_cirrhosis, http://www.merckmanuals.com/professional/hepatic_and_biliary_disorders/fibrosis_and_cirrhosis/primary_biliary_cirrhosis_pbc.html?qt=primary%20biliary%20cirrhosis&alt=sh, https://www.mayoclinic.org/diseases-conditions/primary-biliary-cholangitis-pbc/symptoms-causes/syc-20376874
Xrefs

EFO:0004267

GARD:7459

ICD10CM:K74.3

ICD10CM:K74.5

ICD9CM:571.6

MESH:D008105

NCI:C27167

NCI:C51225

OMIM:PS109720

ORDO:186

SNOMEDCT_US_2023_03_01:1761006

SNOMEDCT_US_2023_03_01:31712002

UMLS_CUI:C0008312

UMLS_CUI:C0023892

Alternateids

DOID:1851

Subsets

DO_rare_slim

NCIthesaurus

Synonyms

biliary liver cirrhosis [EXACT]

cholestatic cirrhosis [EXACT]

chronic nonsuppurative destructive cholangitis [EXACT]

primary biliary cirrhosis [EXACT]

Parent Relationships

is_a liver cirrhosis

is_a autoimmune disease of gastrointestinal tract

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