| Metadata | |
|---|---|
| ID | DOID:12236 | 
| Name | primary biliary cholangitis | 
| Definition | A liver cirrhosis characterized by chronic and slow progressive destruction of intrahepatic bile ducts.  http://www.merckmanuals.com/professional/hepatic_and_biliary_disorders/fibrosis_and_cirrhosis/primary_biliary_cirrhosis_pbc.html?qt=primary%20biliary%20cirrhosis&alt=sh, https://www.mayoclinic.org/diseases-conditions/primary-biliary-cholangitis-pbc/symptoms-causes/syc-20376874, http://en.wikipedia.org/wiki/Primary_biliary_cirrhosis  | 
			    
                        
| Xrefs | 
                                
                                    
                                        
					                        
                                             EFO:0004267 SNOMEDCT_US_2023_03_01:1761006 SNOMEDCT_US_2023_03_01:31712002  | 
                        
| Alternateids | 
                                
                                    
                                        
                                            
                                             DOID:1851  | 
                        
| Subsets | 
                                
                                    
                                        
                                            
                                             DO_rare_slim NCIthesaurus  | 
                        
| Synonyms | 
                                
                                    
                                         biliary liver cirrhosis [EXACT] cholestatic cirrhosis [EXACT] chronic nonsuppurative destructive cholangitis [EXACT] primary biliary cirrhosis [EXACT]  | 
                        
| Parent Relationships | 
                            
			        
                                 is_a liver cirrhosis  | 
                         
| Subclass Logical Relationships | 
                            
	                             has phenotype some Abnormal circulating immunoglobulin concentration  |