Visualize Submit Comment
Metadata
ID DOID:2752
PURL http://purl.obolibrary.org/obo/DOID_2752 Copy
Name glycogen storage disease II
Definition A glycogen storage disease characterized by cardiomyopathy and muscular hypotonia are the cardinal features.
https://pubmed.ncbi.nlm.nih.gov/6360103/
Xrefs

GARD:5714

ICD10CM:E74.02

MESH:D006009

MIM:232300

NCI:C84734

SNOMEDCT_US_2023_03_01:237967002

UMLS_CUI:C0017921

Subsets

DO_rare_slim

NCIthesaurus

Synonyms

acid maltase deficiency [EXACT]

deficiency of glucoamylase [EXACT]

deficiency of maltase [EXACT]

Generalized glycogenosis [EXACT]

Glycogen storage disease 2 [EXACT]

glycogen storage disease type II [EXACT]

Glycogen storage disease, type II [EXACT]

Glycogenosis, type 2 [EXACT]

Lysosomal alpha-1,4-glucosidase deficiency [EXACT]

Pompe disease [EXACT]

Pompe's disease [EXACT]

Parent Relationships

is_a autosomal recessive disease

is_a glycogen storage disease

Subclass Logical Relationships

existence starts during some Infantile onset

has material basis in some autosomal recessive inheritance

Add an item to the term tracker