| Metadata | |
|---|---|
| ID | DOID:8970 |
| PURL | http://purl.obolibrary.org/obo/DOID_8970 Copy |
| Name | subacute sclerosing panencephalitis |
| Definition | A viral encephalitis that has_material_basis_in persistent central nervous system infection of the wild-type measles virus (Morbillivirus hominis) characterized by onset of personality or behavioral changes and intellectual deterioriation years after initial infection, followed by progressive decline in motor function, akinetic mutism or coma, and death. Higher incidence or shorter latency periods may be observed in those initially infected under the age of 2 or in cases of intrafamilial transmission. https://pmc.ncbi.nlm.nih.gov/articles/PMC6450100/, http://en.wikipedia.org/wiki/Subacute_sclerosing_panencephalitis, https://www.ncbi.nlm.nih.gov/books/NBK560673/, https://medlineplus.gov/ency/article/001419.htm, https://doi.org/10.1542/9781610027373-S3_012_002, https://pubmed.ncbi.nlm.nih.gov/14872030/ |
| Xrefs |
SNOMEDCT_US_2025_09_01:192685000 |
| SKOS |
exactMatch ORDO:2806 exactMatch MESH:D013344 exactMatch ICD10CM:A81.1 exactMatch MIM:260470 exactMatch UMLS_CUI:C0038522 exactMatch ICD9CM:046.2 exactMatch GARD:7708 exactMatch NCI:C85171 |
| Subsets |
DO_infectious_disease_slim DO_rare_slim NCIthesaurus |
| Synonyms |
Dawson's encephalitis [EXACT] Dawson's inclusion body encephalitis [EXACT] SSPE [EXACT] subacute sclerosing leukoencephalopathy [EXACT] Van Bogaert's sclerosing leukoencephalitis [EXACT] |
| Parent Relationships |
is_a viral encephalitis |
| Subclass Logical Relationships |
has material basis in some Morbillivirus hominis |