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Metadata
ID DOID:8997
Name polycythemia vera
Definition A myeloproliferative neoplasm characterized by erythroid hyperplasia, myeloid leukocytosis, thrombocytosis, and splenomegaly.
https://en.wikipedia.org/wiki/Polycythemia_vera, https://rarediseases.info.nih.gov/diseases/7422/polycythemia-vera, https://www.mayoclinic.org/diseases-conditions/polycythemia-vera/symptoms-causes/syc-20355850
Xrefs

GARD:7422

ICD10CM:D45

ICD9CM:207.1

ICD9CM:238.4

ICDO:9950/3

MESH:D011087

NCI:C3336

OMIM:263300

SNOMEDCT_US_2023_03_01:154644004

SNOMEDCT_US_2023_03_01:188753004

UMLS_CUI:C0032463

UMLS_CUI:C0152272

Alternateids

DOID:11868

Subsets

DO_cancer_slim

DO_rare_slim

NCIthesaurus

Synonyms

chronic erythremia [EXACT]

Osler-Vaquez syndrome [EXACT]

Polycythaemia rubra vera [EXACT]

Proliferative polycythaemia [EXACT]

Parent Relationships

is_a myeloproliferative neoplasm

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