| Metadata | |
|---|---|
| ID | DOID:9255 | 
| Name | frontotemporal dementia | 
| Definition | A dementia characterized by progressive neuronal loss predominantly involving the frontal and/or temporal lobes of the brain resulting in a gradual and progressive decline in behavior or language.  https://www.rarediseases.org/rare-disease-information/rare-diseases/byID/673/viewAbstract, https://www.ncbi.nlm.nih.gov/pubmed/21121521, http://en.wikipedia.org/wiki/Frontotemporal_dementia, http://www.mayoclinic.org/diseases-conditions/frontotemporal-dementia/basics/definition/con-20023876  | 
			    
                        
| Xrefs | 
                                
                                    
                                        
					                        
                                            
                                            
                                        
                                    
                                
                                    
                                        
					                        
                                            
                                            
                                        
                                    
                                
                                    
                                        
					                        
                                            
                                            
                                        
                                    
                                
                                    
                                        
					                        
                                            
                                            
                                        
                                    
                                
                                    
                                        
					                        
                                             SNOMEDCT_US_2023_03_01:42369001  | 
                        
| SKOS | 
                                
                                    
                                        
                                            
					                            
                                                 exactMatch MESH:D057180  | 
                        
| Subsets | 
                                
                                    
                                        
                                            
                                             DO_FlyBase_slim DO_rare_slim  | 
                        
| Synonyms | 
                                
                                    
                                         frontotemporal lobar degeneration [EXACT] multiple system tauopathy with presenile dementia [EXACT] pallidopontonigral degeneration [EXACT] Wilhemsen-Lynch disease [EXACT]  | 
                        
| Parent Relationships | 
                            
			        
                                 is_a brain disease is_a dementia  | 
                         
| Subclass Logical Relationships | 
                            
	                             disease has location some brain  |